Congenital mesoblastic nephroma

Get in touch with RARE Concierge.

Contact RARE Concierge

Congenital mesoblastic nephroma

A rare renal tumor characterized by a unilateral solitary well demarcated mesenchymal/myofibroblastic neoplasm occurring in very young children. Histopathologically three subtypes (classic cellular and mixed) can be distinguished. The tumor most commonly involves the renal sinus and is typically discovered as a palpable abdominal mass. Patients may also present with hypertension or hematuria rarely with hypercalcemia or hyperreninemia. Prenatal presentation usually with polyhydramnios is not infrequent. The most important prognostic factor is completeness of surgical resection. Overall malignant potential is low and clinical outcome favorable.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

Newly diagnosed with
Congenital mesoblastic nephroma?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


Educate and provide resources to POC with Rare Cancers

Clinical Trials

For a list of clinical trials in this disease area, please click here.