Diencephalic syndrome
Synonyms: Diencephalic cachexia | Diencephalic syndrome of childhood | Diencephalic syndrome of emaciation | Russell diencephalic cachexia | Russell syndrome
Diencephalic syndrome (DS) is a rare condition characterized by profound emaciation and failure to thrive (with normal caloric intake and normal linear growth) hyperalertness hyperkinesia and euphoria in the presence of hypothalamic tumors.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Diencephalic syndrome?
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Clinical Trials
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