Diffuse intrinsic pontine glioma

Get in touch with RARE Concierge.

Contact RARE Concierge

Diffuse intrinsic pontine glioma

Synonyms: DIPG

A rare glial tumor characterized by a highly aggressive diffusely infiltrative pontine lesion generally occurring in children affecting local nerve fiber tracts and spreading contiguously to involve adjacent structures but also metastasizing within the central nervous system. Patients mostly present with a short history of symptoms typically including the classic triad of multiple cranial neuropathies long tract signs and ataxia. Signs and symptoms of increased intracranial pressure may present due to obstructive hydrocephalus. Prognosis is poor and not related to histological grade.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.

Newly diagnosed with
Diffuse intrinsic pontine glioma?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

Pediatric Brain Tumor Foundation

The Pediatric Brain Tumor Foundation (PBTF) leads the way in ending the childhood cancer community’s biggest crisis through research funding, family support and advocacy. Dedicated wholly to addressing this rare, but devastating disease, we are guided by the experiences of patients, survivors, their parents, and siblings.

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


Educate and provide resources to POC with Rare Cancers

Clinical Trials

For a list of clinical trials in this disease area, please click here.