Frontotemporal dementia with motor neuron disease

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Frontotemporal dementia with motor neuron disease

Synonyms: FTD-ALS | FTD-MND | Frontotemporal dementia with amyotrophic lateral sclerosis

Frontotemporal dementia with motor neuron disease (FTD-MND) is a type of frontotemporal lobar degeneration characterized by the insidious onset (between the ages of 38-78 years) of dementia-associated psychiatric symptoms (e.g. personality changes uninhibited behavior irritability aggressiveness) memory difficulties global intellectual impairment emotional disorders and transcortical motor aphasia that eventually leads to mutism in addition to the manifestations of motor neuron disease such as neurogenic muscular wasting (similar to what is seen in amyotrophic lateral sclerosis; see this term). The disease is progressive with death occurring 2-5 years after onset.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

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Advocacy Organizations

patriot for growth and development initiative

Patriots for Growth and Development Initiatives (PGDI), is dedicated to creating a sustainable and equitable world where everyone has access to basic amenities, quality education, decent healthcare, and good livelihoods. Our mission is to promote sustainable development, democracy and good governance, anti-corruption, and accountability, health with a specific focus on rare diseases.

Genetic Support Network of Victoria

The Genetic Support Network of Victoria is an organisation that supports people living with genetic, undiagnosed and rare conditions and those who support them including community and families, patient support organisations, health professionals and industry. Our vision is our community flourishing and living their best lives.

Clinical Trials

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