Ileal neuroendocrine tumor

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Ileal neuroendocrine tumor

Synonyms: Ileal neuroendocrine neoplasm

Ileal neuroendocrine tumor is a rare primary malignant epithelial neoplasm of the small intestine arising from enterochromaffin cells in the ileum (usually the terminal ileum). Clinical behavior depends on the histologic grade but initially it is generally characterized by vague abdominal symptoms (cramping bloating diarrhea) with insidious onset although sometimes it could present with signs of bowel obstruction/perforation or gastrointestinal bleeding. Diagnosis in advanced stages with regional or distant spread is common but signs of carcinoid syndrome (flushing sweating diarrhea) are usually not apparent until hepatic metastasis has occurred.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

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Ileal neuroendocrine tumor?

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Advocacy Organizations

Neuroendocrine Cancer Awareness Network Inc

The Neuroendocrine Cancer Awareness Network (NCAN) is a non-profit organization dedicated to raising awareness of Neuroendocrine Cancer, providing support for caregivers and people with NETs, and funding for NET cancer research. Since 2003, it has been our mission, or as we like to say, our passion, to educate and support the NET community as a whole. That’s our thing.

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


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Clinical Trials

For a list of clinical trials in this disease area, please click here.