Ileal neuroendocrine tumor

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Synonyms: Ileal neuroendocrine neoplasm

Ileal neuroendocrine tumor is a rare primary malignant epithelial neoplasm of the small intestine arising from enterochromaffin cells in the ileum (usually the terminal ileum). Clinical behavior depends on the histologic grade but initially it is generally characterized by vague abdominal symptoms (cramping bloating diarrhea) with insidious onset although sometimes it could present with signs of bowel obstruction/perforation or gastrointestinal bleeding. Diagnosis in advanced stages with regional or distant spread is common but signs of carcinoid syndrome (flushing sweating diarrhea) are usually not apparent until hepatic metastasis has occurred.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version May 2024

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