Inflammatory myofibroblastic tumor

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Inflammatory myofibroblastic tumor is a rare neoplastic lesion of the submucosal stroma which can develop in any organ often occurring in the lung mesentery omentum and the retroperitoneal region. It is histologically heterogenous composed of spindle-shaped cells myofibroblasts and inflammatory cells. It is usually benign however local invasion recurrence malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever malaise weight loss anemia thrombocytosis) or symptoms related to compression of adjacent organs such as bowel obstruction.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


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