Non-functioning neuroendocrine tumor of pancreas
Synonyms: Non-functioning PNET | Non-functioning pancreatic NET | Non-functioning pancreatic neuroendocrine tumor | Non-functioning well-differentiated NEN of pancreas | Non-functioning well-differentiated neuroendocrine neoplasm of pancreas | Non-functioning well-differentiated pancreatic NEN | Non-functioning well-differentiated pancreatic neuroendocrine neoplasm
A rare neuroendocrine tumor of pancreas characterized by a well-differentiated epithelial pancreatic neuroendocrine neoplasm measuring at least 0.5 cm without distinct hormonal syndrome. Tumors <0.5 cm are called microadenomas. Microadenomatosis is the multifocal occurrence of microadenomas. Histopathologic examination shows an organoid growth pattern and expression of synaptophysin and chromogranin A on immunohistochemistry. Tumors are often discovered incidentally or patients may present with symptoms related to local or metastatic tumor spread. Microadenomas are considered benign while larger tumors may behave in a malignant manner with extrapancreatic spread metastasis or recurrence.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Advocacy Organizations
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My Faulty Gene
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My Little Sunshine Foundation
My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.
Neuroendocrine Cancer Awareness Network Inc
The Neuroendocrine Cancer Awareness Network (NCAN) is a non-profit organization dedicated to raising awareness of Neuroendocrine Cancer, providing support for caregivers and people with NETs, and funding for NET cancer research. Since 2003, it has been our mission, or as we like to say, our passion, to educate and support the NET community as a whole. That’s our thing.
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