A rare non-syndromic diaphragmatic or abdominal wall malformation a remnant of omphalomesenteric duct characterized by cuboidal or columnar epithelium with gastrointestinal differentiation. Patients may be asymptomatic or present with infraumbilical mass umbilical lesion with secretions abdominal pain hernia abscess gastrointestinal tract bleeding intestinal obstruction and acute abdomen.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
Newly diagnosed with
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