Pigmented paravenous retinochoroidal atrophy

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Pigmented paravenous retinochoroidal atrophy

Synonyms: PPRCA

Pigmented paravenous retinochoroidal atrophy (PPRCA) is a rare commonly bilateral and symmetric retinal disease characterized by non-progressive or slowly progressive chorioretinal atrophy peripapillary pigmentary changes and accumulation of ”bone-corpuscle” pigmentation along the retinal veins and which is usually asymptomatic or can present with mild blurred vision.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.

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