Primary intralymphatic angioendothelioma

Get in touch with RARE Concierge.

Contact RARE Concierge

Primary intralymphatic angioendothelioma

Synonyms: Dabska tumor

A rare vascular tumor characterized by an ill-defined slowly growing asymptomatic cutaneous plaque or nodule mostly involving the limbs in fewer cases the trunk. The tumor is composed of lymphatic-like channels with prominent intraluminal papillary tufts with hyaline cores lined by hobnail endothelial cells. It is locally aggressive while metastasis is rare. Infants and children are much more often affected than adults.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version March 2024

Newly diagnosed with
Primary intralymphatic angioendothelioma?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Clinical Trials

For a list of clinical trials in this disease area, please click here.