Reticular dystrophy of the retinal pigment epithelium
A rare patterned dystrophy of the retinal pigment epithelium of progressive course characterized by the presence of a bilateral hyperpigmented reticular pattern resembling a fishnet with knots resulting in a slowly progressive loss of vision that often only becomes apparent in old age. This disorder is sometimes associated with scleral staphyloma choroidal neovascularization convergent strabismus spherophakia with myopia and luxated lenses and partial atrophy of the iris.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024
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Reticular dystrophy of the retinal pigment epithelium?
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