Reticulate acropigmentation of Kitamura
Synonyms: RAK
A rare genetic hyperpigmentation of the skin disease characterized by childhood to adulthood-onset of reticulate slightly depressed sharply demarcated brown macular skin lesions without hypopigmentation affecting the dorsa of the hands and feet and occasionally progressing to involve limbs neck forehead and/or trunk. Interrupted dermatoglyphics and palmoplantar pits may be additionally observed. Histologically hyperpigmented lesions show slightly elongated and thinned rete ridges mild hyperkeratosis without parakeratosis and absence of incontinentia pigmenti.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
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Reticulate acropigmentation of Kitamura?
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