Reticulate acropigmentation of Kitamura
Synonyms: RAK
A rare genetic hyperpigmentation of the skin disease characterized by childhood to adulthood-onset of reticulate slightly depressed sharply demarcated brown macular skin lesions without hypopigmentation affecting the dorsa of the hands and feet and occasionally progressing to involve limbs neck forehead and/or trunk. Interrupted dermatoglyphics and palmoplantar pits may be additionally observed. Histologically hyperpigmented lesions show slightly elongated and thinned rete ridges mild hyperkeratosis without parakeratosis and absence of incontinentia pigmenti.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Reticulate acropigmentation of Kitamura?
Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.
Advocacy Organizations
Syndromes Without A Name (SWAN) Australia
Provide information, support and advocacy to families caring for a child with an undiagnosed or rare genetic condition.
Clinical Trials
For a list of clinical trials in this disease area, please click here.