Rosette-forming glioneuronal tumor
Synonyms: RGNT
Rosette-forming glioneuronal tumor is a rare mixed neuronal-glial tumor characterized by the presence of uniform rosette- (or pseudorosette-) forming neurocytes with an astrocytic component together creating a biphasic pattern. It can present with signs of raised intracranial pressure (headache vomiting papilledema) hydrocephalus seizures ataxia and visual disturbances or can be diagnosed incidentally in asymptomatic patients. The tumor usually arises in the midline involving the fourth ventricle or the cerebellum.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Rosette-forming glioneuronal tumor?
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