Synonyms: Secondary pseudohypoaldosteronism | TPHA
A rare renal tubulopathy secondary to urinary tract infection (UTI) and/or urinary tract malformation (UTM) characterized by renal tubular resistance to aldosterone characterized by hyponatremia metabolic acidosis hyperkalemia and inappropriately high serum aldosterone concentration and clinically manifesting as dehydration vomiting and poor oral intake.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version December 2023
Newly diagnosed with
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