Ulerythema ophryogenesis
Ulerythema ophryogenesis is characterised by inflammatory keratotic papules occurring on the face which may be followed by scars atrophy and alopecia. Prevalence is unknown but the disease affecting mainly children and young adults is rare. Erythema with mild hyperkeratosis of the hair follicles resulting in rough papules is observed on the cheeks and lateral aspects of the eyebrows. The disorder occasionally extends to the adjacent scalp ears and forehead and rarely to the extensor surfaces of the limbs. Symptoms regress with age although loss of the lateral aspects of the eyebrows can occur. Many cases occur sporadically; autosomal dominant inheritance has also been reported. There is no particular treatment but patients should avoid sun exposure without UV protection.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Ulerythema ophryogenesis?
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