Atypical coarctation of aorta
Synonyms: Coarctation of the abdominal aorta | Mid-aortic dysplastic syndrome | Mid-aortic syndrome | Midaortic syndrome | Middle aortic syndrome
A rare vascular anomaly characterized by the segmental narrowing of the abdominal and/or distal descending thoracic aorta with varying involvement of the visceral and renal arteries that commonly presents in children and young adults with early onset and refractory hypertension abdominal angina and lower-limb claudication that can lead to life-threatening complications associated with severe hypertension (i.e. myocardial infarction heart failure aortic rupture renal insufficiency and intracranial hemorrhage). It may be due to various congenital or acquired causes but it is most often secondary to an acquired inflammatory disease (i.e. Takayasu arteritis or giant cell arteritis).
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
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Atypical coarctation of aorta?
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Project FAVA is a 501(c)(3) non-profit patient advocacy group that promotes awareness of fibro-adipose vascular anomalies, educates patients, their families, and the global community, and provides helpful resources to those with FAVA. Project FAVA also advances research to move the needle towards more effective and less invasive treatment options for FAVA patients.
Collaborative Research Advocacy for Vascular Anomalies Network (CaRAVAN)
As the research-based umbrella organization for all vascular anomalies, we are on a mission to develop a unified network of patients and their families, advocates, researchers, and clinicians who influence research from initial concept and design to patient care delivery
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