Progressive supranuclear palsy-corticobasal syndrome

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Progressive supranuclear palsy-corticobasal syndrome

Synonyms: PSP-CBS | PSP-corticobasal syndrome

An atypical variant of progressive supranuclear palsy (PSP) a rare late-onset neurodegenerative disease characterized by a variable mixture of progressive asymmetric limb rigidity apraxia cortical sensory loss alien limb dystonia and bradykinesia that is unresponsive to levodopa. Postural instability and axial rigidity develop as the disease progresses. Neuropathological characteristics includes tau pathology and neuronal loss in specific brain areas especially in the midfrontal and inferior parietal cortices.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

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Advocacy Organizations

Genetic Support Network of Victoria

The Genetic Support Network of Victoria is an organisation that supports people living with genetic, undiagnosed and rare conditions and those who support them including community and families, patient support organisations, health professionals and industry. Our vision is our community flourishing and living their best lives.

Clinical Trials

For a list of clinical trials in this disease area, please click here.