Scleromyxedema without monoclonal gammopathy
Scleromyxedema without monoclonal gammopathy is a form of atypical lichen myxedematosus (see this term) characterized by a generalized sclerodermoid infiltration of skin studded with multiple firm papules of 1-3 mm in diameter involving face (leonine appearance) trunk and limbs without monoclonal gammopathy. The involvement of the face can be missing and pruritus may be prominent.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
Newly diagnosed with
Scleromyxedema without monoclonal gammopathy?
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